Abstract:

Objective To explore the clinical pathological features of uterine cystic lymphangioma and promote proper understanding among clinical gynecologists. Methods Clinical manifestations，auxiliary examinations，imaging outcomes，differential diagnosis and treatment of a case of uterine cystic lymphangioma were analyzed，and related literature was reviewed. Results We report the case of a 45-year-old woman hospitalized for intermittent abdominal pain and an abdominal mass. On the basis of these factors，combined with relevant auxiliary examinations，the patient was diagnosed with uterine fibroid cystic change  before the operation.The patient was treated by total hysterectomy，a cystic mass arising from the anterior uterine wall，and clear yellow fluid filled the cyst，while the interior uterine wall is smooth，the uterine cavity is not connected with the cyst. The capsule wall of the tumor was composed of simple squamous cell，lymphatic network structure was obsersed in the smooth muscle of the cystic wall，chamber fibrin content and a few lymphocytes were  also observed. D2-40 was positive，CKpan was weakly positive. The pathological diagnosis was uterus cystic lymphangioma. No special treatment was given after surgery，there was no recurrence at the follow-up of 6 months. Conclusion Uterine adenomyoma cysts are extremely rare and are characterized by abnormal vaginal bleeding and pelvic mass. No features are visible by imaging，serum tumor markers are usually not elevated，and the disease is easily misdiagnosed. Surgery is the treatment of choice，and pathology and immunohistology tests helps to confirm the diagnosis.

Key words: Uterine neoplasms, Uterine cystic lymphangioma, Uterine fibroids cystic degeneration, Misdiagnosis